Health services

Tender description

The service specification for primary ciliary dyskinesia management service (adults) has been developed to support improvement in services for patients with primary ciliary dyskinesia which is genetic condition in which the microscopic cells in the respiratory system called cilia do not function normally. Ciliary dysfunction prevents the clearance of mucous from the lungs, paranasal sinuses and ears. Recurring respiratory infections can lead to an irreversible scarring and obstruction in the bronchi (bronchiectasis) and severe lung damage. Cilia are also present in the ventricles of the brain and in the reproductive system so ciliary dysfunction can also affect other body systems. The service model is described in the service specification 1637 for primary ciliary dyskinesia management service (adults) approved by NHS England and published on the NHS England website https://www.england.nhs.uk/publication/adult-primary-ciliary-dyskinesia-service-specification/ The service specification for primary ciliary dyskinesia management service (adults) has been developed to support improvement in services for patients with primary ciliary dyskinesia which is genetic condition in which the microscopic cells in the respiratory system called cilia do not function normally. Ciliary dysfunction prevents the clearance of mucous from the lungs, paranasal sinuses and ears. Recurring respiratory infections can lead to an irreversible scarring and obstruction in the bronchi (bronchiectasis) and severe lung damage. Cilia are also present in the ventricles of the brain and in the reproductive system so ciliary dysfunction can also affect other body systems. The service model is described in the service specification 1637 for primary ciliary dyskinesia management service (adults) approved by NHS England and published on the NHS England website https://www.england.nhs.uk/publication/adult-primary-ciliary-dyskinesia-service-specification/